Adrenal ganglioneuroma
A case report
DOI:
https://doi.org/10.29193/RMU.36.3.11Keywords:
GANGLIONEUROMA, ADRENALECTOMY, ADRENAL GLAND DISEASESAbstract
Introduction: adrenal ganglioneuroma is an exceptional benign tumour which originates from neural crest cells. The study aims to inform about a clinical case of asymptomatic right adrenal ganglioneuroma.
Clinical case: 37-year old patient, female, who consulted for non-specific abdominal pain which, after imaging assessment and functional and hormone test was diagnosed with non-functioning tumour of the right adrenal gland. Upon this diagnosis, adrenalectomy using the conventional retroperitoneal approach was performed, and the pathology study of the piece confirmed the diagnosis of ganglioneuroma.
Discussion: ganglioneuromas are usually asymptomatic and non-functioning, so diagnosis is incidental in
a large percentage of cases. Others present non-specific symptoms. Preoperative etiological diagnosis is rare, and confirmation is usually after pathology study. Symptomatic tumours over 6cm long have an indication of surgery, as well as those suspicious of malignancy. Prognosis is good, relapses being exceptional.
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