Hipertensión pulmonar tromboembólica crónica

Juan Pablo Salisbury; Pablo Curbelo; Mercedes Arcaus; Jorge Cáneva

Authors

Juan Pablo Salisbury Universidad de la República, Facultad de Medicina, Hospital Maciel, Cátedra de Neumología. Asistente
Pablo Curbelo Universidad de la República, Facultad de Medicina, Hospital Maciel, Cátedra de Neumología. Profesor Adjunto
Mercedes Arcaus Universidad de la República, Facultad de Medicina, Hospital Maciel, Cátedra de Neumología. Asistente
Jorge Cáneva Argentina, Buenos aires. Fundación Favaloro, Universidad Favaloro, Departamento de Clínica Médica. Profesor Titular

Keywords:

PULMONARY HYPERTENSION, THROMBOEMBOLISM, CHRONIC DISEASE

Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is an unusual entity that may be observed in up to 4% of patients surviving an acute pulmonary thromboembolism (APTE). It is a disease with a poor prognosis unless there is an early diagnosis and a timely treatment. Paradoxically, it is the only form of pulmonary hypertension that may be cured by means of a pulmonary endarterectomy (PE). It is initially diagnosed by non-invasive methods such as the Doppler echocardiogram and the ventilation/perfusion pulmonary scintigraphy (V/Q). Diagnostic and preoperative assessment is completed with a right cardiac catheterization and a pulmonary angiography. These techniques confirm the chronic thromboembolic pulmonary hypertension and define whether it is possible to perform a pulmonary endarterectomy.

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