Poliquistosis renal autosómica dominante

Necesidad de diagnóstico y tratamiento oportuno

  • Diego Tobal Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Centro de Nefrología. Profesor Adjunto
  • Oscar Noboa Universidad de la República, Facultad de Medicina, Hospital de Clínicas, Centro de Nefrología. Profesor
Palabras clave: RIÑÓN POLIQUÍSTICO AUTOSÓMICO DOMINANTE

Resumen

La poliquistosis renal autosómica dominante es la enfermedad hereditaria renal más frecuente. Actualmente se están realizando claros avances en el intento de enlentecer su progresión. Con la evidencia actual es aconsejable la detección y el tratamiento precoz de la hipertensión arterial, de los factores de riesgo cardiovascular y de las complicaciones renales y extrarrenales. Se deben aplicar todas las medidas de nefroprevención para evitar la progresión de la enfermedad renal crónica y ofrecer de manera coordinada, en caso de ser necesario, el acceso a todas las técnicas de reemplazo de la función renal, incluido el trasplante renal. Si bien no hay evidencia acerca de la medicación antihipertensiva ideal, el uso de inhibidores de la enzima convertidora de la angiotensina y/o antagonistas de los receptores de la angiotensina II, parece recomendable.

Citas

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Publicado
2014-09-30
Cómo citar
1.
Tobal D, Noboa O. Poliquistosis renal autosómica dominante. Rev. Méd. Urug. [Internet]. 30 de septiembre de 2014 [citado 12 de agosto de 2020];30(3):184-92. Disponible en: http://revista.rmu.org.uy/ojsrmu311/index.php/rmu/article/view/243
Sección
Trabajos de Revisión o Actualización y Puestas al día